Dental Management of a Patient with Spinal Muscular Atrophy under Total Intravenous Anesthesia: A Case Report
조혜진, 김현태, 송지수, 신터전, 현홍근, 김정욱, 장기택, 김영재,
소속 상세정보
조혜진 ( Cho Hye-Jin ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김현태 ( Kim Hyun-Tae ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
송지수 ( Song Ji-Soo ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
신터전 ( Shin Teo-Jeon ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
현홍근 ( Hyun Hong-Keun ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김정욱 ( Kim Jung-Wook ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
장기택 ( Jang Ki-Taeg ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
김영재 ( Kim Young-Jae ) - Seoul National University School of Dentistry Department of Pediatric Dentistry
KMID : 1144020210170020033
Abstract
Spinal muscular atrophy (SMA) is an autosomal recessive neuromuscular disease caused by mutations in the survival of motor neurons (SMN1) gene, located on chromosome 5q13. It affects 1 in 6,000 to 1 in 10,000 live births and is characterized by degeneration of lower motor neurons in the anterior horn in the spinal cord, resulting in muscle weakness and atrophy. Special care must be taken during general anesthesia due to weak respiratory muscles and hypersensitivity to muscle relaxants. This report describes dental treatment of a 6-year-11-months old boy with SMA type II under total intravenous anesthesia using propofol and remifentanil without the use of muscle relaxant. The patient exhibited malocclusions related to weak masticatory muscles and mouth breathing. Dental caries treatment with composite resin restoration and surgical extraction of impacted mesiodens was performed without any postoperative complications. The patient recovered fully from general anesthesia and was discharged on the day without the need of hospitalization.
키워드
Spinal muscular atrophy; Total intravenous anesthesia; Dental treatment
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